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| Product Range | Methionine100 |
| Pack Size | 30 x 4g ℮ |
| Ingredients | Dried glucose syrup, L-methionine. |
Clinical Use
Remethylation disorders1
Remethylation defects are rare inherited disorders in which a deficient activity of methionine synthase results in impaired remethylation of homocysteine to L-methionine, leading to the accumulation of homocysteine and decreased L-methionine levels.
Although remethylation disorders affect multiple systems, and thus often presents in a multifaceted manner, a few patterns of clinical presentations can be identified. These include developmental and neurocognitive impairment, feeding problems, neurological symptoms including seizures, movement disorders, abnormal muscle tone, visual impairment, neuropathy and haematological abnormalities.
L-methionine is an essential amino acid. Maintaining plasma levels in the normal range is recommended and can be achieved by oral L-methionine supplementation where necessary.
Preparation Guidelines
To be determined by the clinician or dietitian. Suggested methods include:
