Product Range | Glycine500 |
Pack Size | 30 x 4g ℮ |
Ingredients | Maltodextrin, Glycine. |
Clinical Use
Serine deficiency disorders1
Serine deficiency disorders are neurometabolic disorders caused by a defect in one of the three synthesizing enzymes of the L-serine biosynthesis pathway. Congenital microcephaly, seizures and severe psychomotor retardation are all symptoms of serine deficiency. As glycine can be synthesized directly from L-serine and vice versa, L-serine deficiency disorders tend to also present with low or low to normal glycine concentrations.
Supplementing the diet with L-serine and glycine can help address potential deficiencies and may improve clinical outcomes.
Preparation Guidelines
To be determined by the clinician or dietitian. Suggested methods include:
Further Reading
1. De Koning TJ. Treatment with amino acids in serine deficiency disorders. Journal of Inherited Metabolic Disease 2006:29(2-3); 347-351. https://doi.org/10.1007/s10545-006-0269-0
Glycine500 is a Food for Special Medical Purposes for the dietary management of inborn errors of metabolism. For use under medical supervision. For healthcare professional use only.