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| Product Range | Citrulline200 | Citrulline1000 |
| Pack Size | 30 x 4g ℮ | 30 x 4g ℮ |
| Ingredients | Maltodextrin, L-citrulline. | Maltodextrin, L-citrulline. |
Clinical Use
Urea Cycle Disorders1 (UCD)
UCD is an umbrella term encompassing six genetic disorders of protein metabolism, all of which result in impairment of the body’s ability to remove waste nitrogen. UCD can have acute, chronic and intermittent clinical manifestations occurring at any age. Their clinical hallmark is the hyperammonaemia crisis.
Due to impaired synthesis, L-arginine becomes an essential amino acid in all of the UCDs, with the exception of Arginase 1 deficiency. It must therefore be supplemented as either L-arginine or its precursor, L-citrulline. In some of the UCDs, low plasma levels of L-citrulline are found. Supplementing the diet with L-citrulline will help manage both low L-citrulline and low L-arginine levels.
Preparation Guidelines
To be determined by the clinician or dietitian. Suggested methods include:
